Arrhythmogenic cardiomyopathy (AC) is a rare inherited heart muscle condition that causes irregular heart rhythms (arrhythmias) at a higher rate than other heart muscle conditions. AC can affect primarily either the left ventricle (Left Dominant Arrhythmogenic Cardiomyopathy) or the right ventricle (Arrhythmogenic Right Ventricular Cardiomyopathy or ARVC). Individuals with AC or ARVC may have symptoms of palpitations or fainting due to arrhythmias. Symptoms may also include shortness of breath due to reduced pumping function of the heart.
Medical Services related to Adam Steven Helms MD
Brugada Syndrome is an inherited arrhythmia syndrome that affects 1 out of 5000 in the population. It is caused by abnormal electrical recharging of the heart, most commonly due to abnormal channels in heart muscle cells that control the flow of sodium. Individuals with Brugada Syndrome may have symptoms from abnormal heart rhythms (arrhythmias), including palpitations, fainting or seizures. Arrhythmias often occur at times of rest or with fevers, and affect men more seriously than women. There is a large amount of variability in the risk of arrhythmias among individuals with Brugada Syndrome, even within the same family. Evaluation of the whole family is important since the condition is often passed on to the next generation of a family but may not cause symptoms initially.
CPVT, or Catecholaminergic Polymorphic Ventricular Tachycardia, is an inherited arrhythmia syndrome that affects 1 out of 5,000 in the population. It is caused most commonly by abnormal control of calcium movement in heart muscle cells. Individuals with CPVT may have symptoms from abnormal heart rhythms (arrhythmias), including palpitations, episodic lightheadedness, or fainting episodes.
Dilated cardiomyopathy, or DCM, is a heart muscle condition characterized by gradual weakening of the heart muscle. While DCM may be caused by other conditions, including myocardial infarction, many cases are now known to be caused by genetic mutations carried in families. Individuals with DCM may be only mildly affected or may be severely affected, even in the same family.
Hypertrophic cardiomyopathy (HCM) is a common genetic cardiac disorder affecting 1 in 500 people. It affects both men and women of all ages, and is characterized by abnormal thickening of the heart muscle.
The Michigan Medicine Frankel Cardiovascular Center and the Michigan Congenital Heart Center at C.S. Mott Children's Hospital offer established, comprehensive programs for the evaluation and treatment of inherited heart conditions (cardiomyopathies) and arrhythmias from child to adult. Our program is one of only 24 in the country specializing in the treatment of these conditions.
Long QT syndrome is an inherited arrhythmia syndrome that affects 1 out of 2000 in the population. It is caused by longer electrical recharging of the heart after each heart beat. This longer recharging time is most commonly due to abnormal channels in heart muscle cells that control the flow of potassium and sodium electrolytes.