Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC)

What is ARVC?

Illustration of ARVC showing enlarged right ventricle of the heart

Arrhythmogenic right ventricular cardiomyopathy is a rare inherited heart muscle condition that most often involves the right ventricle, which is the heart chamber responsible for pumping blood to the lungs. Individuals with ARVC may have symptoms of palpitations or fainting due to irregular heart rhythms (arrhythmias).  Symptoms may also include shortness of breath due to reduced pumping function of the heart.

Evaluation of the whole family is important since the condition is often passed on to the next generation of a family but may not cause symptoms initially. The diagnosis of ARVC is often challenging and requires a thorough evaluation, including advanced imaging with cardiac MRI and genetic testing. Careful risk assessment for dangerous arrhythmias is also an important part of the evaluation, and sometimes implantable defibrillators (ICDs) are recommended in high risk individuals. High intensity exercise or sports may contribute to worsening in some patients, and thoughtful, personalized counseling to set exercise guidelines is often needed. While no medications are known to prevent worsening of ARVC, with correct identification of individuals at high-risk of arrhythmias, many people with ARVC lead full and normal lives.

Our ARVC program offers expertise in the clinical evaluation of ARVC in children and adults, knowledgeable use of genetic testing, genetic counseling, advanced cardiac imaging, evaluation of arrhythmia risk, and defibrillator implantation when needed. 

Learn more about Inherited Cardiomyopathies and Arrhythmias and our Inherited Cardiomyopathies and Arrhythmias Team.

Patient Resources

Make an Appointment

To make an appointment to discuss your need for cardiomyopathy treatment:

  • Adult: Call 1-888-287-1082 or email us at
  • Pediatric: Call 1-734-5176
  • Physician Referrals: To refer a patient, call M-Line, 1-800-962-3555